一个宝宝，刚出生4天，手和脚都没有覆盖皮肤，鲜红的皮下组织直接裸露出来。另一个宝宝，从出生起手和脚就开始发水疱，然后溃破，让人不忍心多看……最近一周内，湖南省人民医院新生儿科，先后接收了这两个分别来自益阳和衡阳的新生男婴。因为转院匆忙，他们连名字都没来得及取。

A baby,Just was born four days,Hands and feet are not covered the skin,Bright red subcutaneous tissue directly exposed out.Another baby,From birth hands and feet began to send blisters,Then run broken,Let a person can't bear to see...Recently a week,Hunan province people's hospital of pediatrics freshmen,Has received the two respectively yiyang and hengyang from the new born baby.Because the hospital in a hurry,They even didn't name could take.

　　省人民医院新生儿科请来了皮肤科、烧伤整形科专家进行会诊，初步判断他们患的是一种名叫“遗传性大疱表皮松解症”的病。根据教科书记载，这种疾病发病率仅为十万分之二，临床上十分罕见。11月21日，省人民医院新生儿科主任张爱民介绍，由于身体皮肤及口腔黏膜缺损，对外界环境没有屏蔽能力，这两个宝宝极易受到感染，所以精心护理格外重要。即便幸运闯过了目前的“感染关”，未来的四肢功能和行走活动都将受到影响。

Provincial people's hospital, a new pediatric dermatology/Burn ZhengXingKe experts consultation,The initial judgment they had a name"Hereditary bullosa epidermolysis disorder"disease.According to the book records,The disease incidence rate is only two over one hundred thousand,Clinical go up is very rare.On November 21st,Province people's hospital of pediatrics director of new ZhangAiMin is introduced,Due to the body skin and oral mucosa defect,On the outside environment is not shielding ability,The two baby vulnerable to infection,So careful nursing are especially important.Even if lucky break through the current"Infection shut",The future of limb function and walk activities will be affected.

　　隔着病房的玻璃窗可以看到，为了预防感染，医护人员都得仔细洗手消毒，把口罩、帽子、手套都戴齐全，再穿好隔离服后才能接近患儿。每隔几个小时，护士就会把烧伤药膏涂抹在患处，再用纱布包裹起来。据悉，其中有对父母已经对治愈不抱太大希望，已经把宝宝接回了老家。张爱民说，如果他们打算再要个孩子，一定得先到医院接受遗传学相关分析和检查，才可以避免再次出现类似情况。

Across the ward Windows can see,In order to prevent infection,Medical staff have to careful hand washing,The mask/hat/Gloves all wear is complete,Wear it again good isolation suit to close to the children.Every few hours,The nurse will burn ointment daub on the affected part,Garnish with gauze wrap up.It is reported,There are to parents have to heal not very hopeful,Has the baby after back to the hometown.ZhangAiMin said,If they are going to want again to a child,Must go to hospital for genetic correlation analysis and inspection,To avoid similar situation appear again.

　　(潇湘晨报 记者 张莹 通讯员 梁辉)

(Xiaoxiang morning paper reporter correspondent ZhangYing liou j w)