出生20天宝宝遭遇“吸血鬼” 原来是肿瘤作祟 The baby was born 20 days encounter"vampire" It is the tumor haunt

原来是“吸血”肿瘤作祟 专家冒险为其切除保住腿 It is"vampire"Tumor haunt experts adventure for the resection of keep leg

　　一个才出生20天的宝宝，右腿在一晚上变得比左腿粗了一倍，占到了全身体重的一半。这一切，只因宝宝患上了一种怪病，这种病就像是被吸血恶魔附身一样会不断被“吸血”，宝宝身上三分之一的血液被这个瘤子吸走了。宝宝随时有可能大出血死亡，在这危急关头，南京市儿童医院专家决定冒险为他切除肿瘤。

A baby born 20 days,The right leg in a night becomes much smaller than the left leg coarse a times,Accounted for half of the body weight.All this,Because the baby had a strange disease,This kind of disease is like a vampire is evil spirit will constantly be"vampire",The baby, a third of blood is the tumour suction go.The baby whenever possible hemorrhea death,In this critical moment,Nanjing children's hospital experts decided to take the plunge and for him to remove the tumor.

一夜间肿瘤就弥漫了宝宝下半身 The tumor is pervaded the overnight baby the lower half

　　这个小宝宝就是钱先生家刚刚迎来的小王子，孩子出生后，医生就告诉钱先生小宝宝的腿上长出一个血管瘤，建议等孩子长大些再动手术。钱先生看到这个瘤子还比较小，而且孩子那么小就要动手术，实在狠不下心来。“坏就坏在我的心软，在宝宝出生后的几天，瘤子就开始慢慢地变大了。”钱先生说。更严重的情况出现在住院前的一天，那天钱先生晚上睡觉前专门看了一下孩子右腿上的“小瘤子”，但是第二天早上钱先生惊奇地发现孩子不单是右腿，右侧的腹股沟也变了颜色肿胀起来。

The baby is Mr. Qian has welcomed home the little prince,After the child is born,The doctor will tell Mr Qian baby legs grow a hemangioma,The child grew some proposals to perform an operation.We see the tumour is relatively small,Children so small and will perform an operation,Really not malicious heart to."The bad is bad in my softhearted,In the days after the birth of a new baby,Tumors began to slowly go big."Mr Qian said.A more serious situation in hospital a day before,The day before he goes to bed at night we specially looked at the children on the right leg"Small tumors",But the next morning after he was surprised to discover the child is not only the right leg,On the right side of the inguinal also changed color swelling up.

　　孩子被送到南京市儿童医院，经过烧伤整形科的沈卫民主任初步判断他可能是得了一种恶性肿瘤，经过进一步的检查后，医生发现这个小宝宝的血小板居然只有4×109/L，而且血色素只有4g，而正常人血小板范围应该保持在100×109/L-300×109/L，血色素为10g以上。如此低的血小板让孩子出现的任何一个小伤口，都可能因为无法正常凝血，形成致命伤害。难道孩子的病情另有隐情？沈主任为此翻阅了大量的参考文献，并和自己的团队展开了数次讨论。最后，沈主任确诊孩子的肿瘤为KM综合征血管内皮瘤，是一种罕见的血管瘤综合征，该病最大的特征就是“吸血”。

Children were sent to nanjing children's hospital,After burn ZhengXingKe ShenWei of democracy as the initial judgment he may have a malignant tumor,After further examination,The doctor found the baby of platelet incredibly only 4 x 109 / L,And hemoglobin only 4 g,And normal platelet range should keep in 100 x 109 / L - 300 x 109 / L,Hemoglobin for more than 10 g.So low platelet let children appear anywhere on a small wound,May be because can't normal blood coagulation,Formation lethal damage.Is the child's illness otherwise than that?Shen director to browse through a large number of references,And his team launched several times to discuss.finally,Shen, director of the children's cancer diagnosis for KM syndrome hemangioendothelioma,Is a rare hemangioma syndrome,The disease is the greatest feature of the"vampire".

体内1/3的血液流进了宝宝右腿 The body a third of the blood flow into the baby's right leg

　　KM综合征全称为Kasabach-Merritt综合征，翻译过来是血管瘤和血管畸形伴发血小板减少综合征，临床表现为迅速增大的血管瘤合并血小板减少、溶血性贫血，急性或慢性弥漫性血管内凝血。这种肿瘤内血管密布，更可怕的是，在肿瘤内有很多的血窦，这些血窦就像吸引器一样，不停把孩子身上的血液、血小板和凝血因子“吸引”到肿块内，孩子如不及时治疗，会出现贫血症状，继而会出现内出血，直至死亡。“以前这种疾病非常少见，一年能见到1-2例，但是最近几年明显多了起来，有时一年可以接诊20多例。”沈卫民主任说。而此时一个难题摆在了沈主任的面前，孩子现在的凝血功能如此之差，手术后根本无法凝血，而且，孩子的这个瘤还在不停地长大，“孩子的两条腿放在一起明显的不一样粗细，左腿只有16cm粗，而右腿已经达到了24cm，一条腿的重量等于孩子其他身体部位的重量。可以说孩子体内1/3的血液都跑到了腿上，必须马上手术。”

KM syndrome all called Kasabach - Merritt syndrome,Translating is hemangioma and vascular malformation accompanying thrombocytopenia syndrome,The clinical manifestations of the rapid increase of hemangioma merger thrombocytopenia/Hemolytic anemia,Acute or chronic diffuse intravascular coagulation.This tumor is within blood vessels,Is more terrible,There were a lot of the tumor blood sinus,These blood sinus like as attractor,Keep children's blood/Platelet and blood coagulation factor"attract"To bump in,The child if not treated in time,Will appear anemia symptoms,Then will appear hemorrhage,Until death."Before this kind of disease is very rare,One year to see 1-2 cases,But in recent years significantly more up,Sometimes a year can accepts more than 20 cases."ShenWei democracy as said.When a problem in the front of the director shen,Children now of coagulant function is so poor,Surgery can't clotting,and,The child's this tumor is constantly to grow up,"The child's legs together obvious different thickness,Left leg only 16 cm thick,And right leg has reached a 24 cm,A leg is equal to the weight of the children of the other parts of the body weight.Can say children body 1/3 of the blood ran on the leg,Must be immediately surgery."

为了孩子的幸福坚决不能截肢 In order to the child's happiness resolute can't amputation

　　孩子的血小板如此低，手术的时候如果出现大出血将是致命的，沈主任为此制定了两套手术方案：一、将肿块周围的血管进行“扎口”，然后将肿块切除；二、直接截肢。但是面对着还是新生儿的小家伙，沈主任坚决地将第二套方案弃用。“肿瘤内部血管很多，有些还同主血管相连，稍有不慎就会造成无法挽回的大出血，所以术前，我们必须大量地为孩子补充血浆、冷沉淀等血液制品提高孩子的凝血功能，术中还要先把肿瘤周围主要动脉和回流静脉一针一针地缝合，然后才进行手术。”沈主任说。经过沈主任的努力孩子的腿保住了，由于术前准备工作比较充分，手术很顺利，孩子腿上的肿瘤切除了2/3,另外的一些残余组织，要经过化疗才能完全清除。

The child's platelet is so low,Surgery if appear hemorrhage can be fatal,Shen director have developed two sets of operation scheme:a/Will bump the blood vessels were around"tying",Then the excision;two/Direct amputation.But face or neonatal little thing,Shen director firmly take the second set of scheme deprecated."The tumor blood essels many,Some are connected with the main blood vessels,Have a little bit the immodesty can cause irreparable hemorrhea,So preoperative,We must massively supplement for children in the plasma/Cold such as precipitation of blood products improve the child's blood clotting,Intraoperative also first around tumor main artery and vein reflux a needle stitch suture,And then an operation."Shen director said.After shen director of the children's efforts to keep the legs,Due to the relatively full preoperative preparation work,Surgery very well,Children on the legs of the two-thirds of tumor resection,Another some residual organization,To pass chemotherapy can be perfectly clear.

　　最后沈主任告诉记者，由于这种病的发病机理不明确，所以预防比较困难，而且近来发病率明显上升，像这样严重的吸血瘤子，最近该院已治疗了好几例。现在医学发达了，许多看似奇怪的病，已经有了比较有效的治疗手段，所以孩子得病后要及时治疗，不能轻言放弃！(据南京晨报)

Finally shen director told reporters,Because of this disease pathogenesis is not clear,So to prevent more difficult,And the recent incidence increased obviously,Like such a serious vampire tumors,Recently the hospital treatment has several cases.Medicine developed now,Many seemingly strange disease,Have more effective treatments,So the child sick after timely treatment,Can't give up!(According to the nanjing morning paper)